Congenital TB has varied clinical manifestations, and may mimic septicaemia in neonates. Congenital TB is transmitted through the infected placenta via the umbilical vein or inhalation and ingestion of infected amniotic fluid. Endometrial TB usually manifests as infertility; however, congenital TB can be identified in the presence of asymptomatic maternal endometrial TB. We report a case of congenital TB associated with asymptomatic maternal endometrial TB to highlight the need for endometrial biopsy in such cases.