Intrasphenoidal Rathke's cleft cyst

J Clin Neurosci. 2015 Oct;22(10):1678-82. doi: 10.1016/j.jocn.2015.05.001. Epub 2015 Jun 26.

Abstract

We report a rare patient with an intrasphenoidal Rathke's cleft cyst (RCC) and review the literature. RCC are benign epithelium lined cysts containing mucoid material, which typically occur in a location that is either entirely intrasellar, or intrasellar with suprasellar extension (intra-suprasellar). RCC in a completely extrasellar location are uncommon. An intrasphenoidal RCC is extremely rare with only two patients reported in the literature to date. Preoperative diagnosis is difficult due to the uncommon location and absence of any characteristic radiological features. However, it remains of utmost clinical relevance because it may limit the operative management to biopsy sampling of the cyst wall and drainage of the contents via the transsphenoidal route.

Keywords: Craniopharyngioma; Radiology; Rathke’s cleft cyst; Sphenoid.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Central Nervous System Cysts / diagnosis*
  • Central Nervous System Cysts / surgery*
  • Humans
  • Male
  • Sphenoid Sinus / pathology*
  • Sphenoid Sinus / surgery*
  • Young Adult