[A case of childhood Behcet's disease with multiple arterial vascular lesions as the first manifestation]

Zhonghua Er Ke Za Zhi. 2024 May 2;62(5):476-477. doi: 10.3760/cma.j.cn112140-20231030-00335.
[Article in Chinese]

Abstract

患儿 女,11岁3月龄,因反复下肢疼痛3个月入院,病程期间出现口腔溃疡、眼部溃疡及便血现象。血管彩色多普勒超声示左侧锁骨下动脉近心段管壁增厚,下肢动脉彩色多普勒超声示双侧股动脉局部管壁增厚,双侧胫后动脉中远段重度狭窄伴节段性闭塞,双侧胫前动脉狭窄可能。电子结肠镜检查示回肠末端、盲肠及乙状结肠、直肠黏膜血水肿,散在多发糜烂和浅溃疡形成。给予醋酸泼尼松片及环磷酰胺,3周后双下肢疼痛缓解,可正常行走,足部溃疡逐渐好转,随访1年后全身血管超声均未见异常。.

Publication types

  • Case Reports

MeSH terms

  • Behcet Syndrome* / complications
  • Behcet Syndrome* / diagnosis
  • Child
  • Cyclophosphamide / administration & dosage
  • Cyclophosphamide / therapeutic use
  • Femoral Artery / diagnostic imaging
  • Femoral Artery / pathology
  • Humans
  • Male
  • Subclavian Artery / diagnostic imaging
  • Subclavian Artery / pathology
  • Ultrasonography, Doppler, Color

Substances

  • Cyclophosphamide