Abstract
患儿 女,11岁3月龄,因反复下肢疼痛3个月入院,病程期间出现口腔溃疡、眼部溃疡及便血现象。血管彩色多普勒超声示左侧锁骨下动脉近心段管壁增厚,下肢动脉彩色多普勒超声示双侧股动脉局部管壁增厚,双侧胫后动脉中远段重度狭窄伴节段性闭塞,双侧胫前动脉狭窄可能。电子结肠镜检查示回肠末端、盲肠及乙状结肠、直肠黏膜血水肿,散在多发糜烂和浅溃疡形成。给予醋酸泼尼松片及环磷酰胺,3周后双下肢疼痛缓解,可正常行走,足部溃疡逐渐好转,随访1年后全身血管超声均未见异常。.
MeSH terms
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Behcet Syndrome* / complications
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Behcet Syndrome* / diagnosis
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Child
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Cyclophosphamide / administration & dosage
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Cyclophosphamide / therapeutic use
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Femoral Artery / diagnostic imaging
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Femoral Artery / pathology
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Humans
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Male
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Subclavian Artery / diagnostic imaging
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Subclavian Artery / pathology
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Ultrasonography, Doppler, Color